Síndrome de Zinner Online (Zinner Syndrome)

¨Cistos congênitos da vesícula seminal (CSVCs) associados a anomalias do trato urinário superior ipsilateral são incomuns. Essa condição foi relatada como “síndrome de Zinner” (ZS) e é considerada a contraparte masculina da síndrome de Mayer-Rokitansky-Kuster-Hauser. O ZS pode ser assintomático e relatado incidentalmente ou pode estar associado a sintomas inespecíficos, como disúria, infecções do trato urinário (ITU), disfunção da bexiga e infertilidade. Quando sintomática, se da pelo tamanho do cisto da vesícula seminal (maior que 5 cm). O diagnóstico exige ser alcançado na idade pediátrica, pois é realizado principalmente na idade adulta, durante o período da atividade sexual. O tratamento de CSVCs é necessário se houver sintomas, pois a abordagem cirúrgica é desafiadora. Além disso, a cirurgia está associada a muitas complicações, devido à localização profunda das vesículas seminais e à dissecção exigente dos cistos no espaço retrovesical.¨

■ Zinner syndrome in pediatric age: issues in the diagnosis and treatment of a rare malformation complex

V Cascini, D Di Renzo, V Guerriero, et al

Front Pediatr 2019, vol 7: 129

https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6465625/

■ Incidental finding of Zinner syndrome in a Greek military recruit: a case report of a rare clinical entity

Evangelos N. Symeonidis, Chrysovalantis Gkekas, Ioannis Tsifountoudis et al

Mil Med Res. 2019; 6: 4.

https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6375168/

■ Zinner syndrome mimicking bladder outlet obstruction managed with aspiration

Ronal Kori, Lovenish Bains, Pawan Lal, Swati Gupta

Urol Ann. 2019 Oct-Dec; 11(4): 449–452

https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6798291/

■ The association of renal agenesis and ipsilateral seminal vesicle cyst: Zinner syndrome case report

Mishal AlArifi, Magdi Al-Gahwary, Mohamed Gomha

Case Rep Urol. 2019; 2019: 1242149

https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6612404/

■ Zinner syndrome presenting with intermittent scrotal pain in a young man

S Florim, V Oliveira, D Rocha

Radiol Case Rep 2018, vol13 (6):12224-1227

https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6148829/

■ Robot-assisted excision of congenital mega-seminal vesicle asociated with Zinner´s syndrome

C F Bryson, S Delpe, S Tatzel et al

Journal of Endoneurology Case Reports 2018, vol 4 (1)

https://www.liebertpub.com/doi/10.1089/cren.2018.0047

■ Zinner syndrome diagnosed by magnetic resonance imaging and computed tomography: role of imaging to identify and evaluate the uncommon variation in development of the male genital tract

Fiaschetti, L. Greco, V. Giuricin et al

Radiol Case Rep. 2017 Mar; 12(1): 54–58

https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5310246/

■ Zinner syndrome: an unusual cause of bladder outflow obstruction

S Shah, R Patel, R Sinha, M Harris

BJR Case Reports 2017, vol 3 (2)

https://www.birpublications.org/doi/full/10.1259/bjrcr.20160094

■ Zinner syndrome – a rare developmental anomaly ot the mesonephric duct diagnosed on magnetic resonance imaging

S Mehra, R Ranjan, U C Garga

Radiol Case Rep 2016, vol 11 (4): 313-317

https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5128193/

■ Zinner´s syndrome: report of two cases and review of the literature

A Slaoui, S Regragui, A Lasri et al

Basic Clin Androl sep 2016

https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5028972/

■ Síndrome de Zinner en paciente afecto de síndrome de Kallmann: rara asociación de 2 malformaciones embrionárias

A Dominguez, M Abascal-Junquera, J Muñoz-Rodriguez, J M Banús

Revista Internacional de Andrologia 2016, vol14 (4)

https://www.elsevier.es/es-revista-revista-internacional-andrologia-262-articulo-sindrome-zinner-paciente-afecto-sindrome-S1698031X16000224

■ Endourologic intervention for management of infertility in a man with Zinner syndrome resulting in a natural pregnancy

Ismaeel Aghaways, Shyaw M. Ahmed

J Endourol Case Rep. 2016; 2(1): 71–73

https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4996586/

■ Renal-type clear cell carcinoma occurring in the prostate with Zinner syndrome

Yuichi Sato, Masao Kataoka, Junya Hata et a

Urol Case Rep. 2016 Mar; 5: 9–12

https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4719893/

■ Congenital seminal vesicle cyst and ipsilateral renal agenesis (Zinner syndrome): a rare association and its evolution from early childhood to adolescence

Aikaterini Kanavaki, Isabelle Vidal, Laura Merlini, Sylviane Hanquinet

European J Pediatr Surg Rep. 2015 Dec; 3(2): 98–102

https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4712056/

■ Zinner syndrome: na uncommon cause of painful ejaculation

Raghav Sundar, Gaurav Sundar

BMJ Case Rep. 2015; 2015: bcr2014207618

https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4368968/

■ It´s not always varicocele: A strange case of Zinner syndrome

Nicola Pavan, Stefano Bucci, Giorgio Mazzon et a

Can Urol Assoc J. 2015 Jul-Aug; 9(7-8): E535–E538.

https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4514510/

■ Síndrome de Zinner: relato de caso clínico