Guidelines on red transfusion in sickle cell disease – Part I: principles and laboratory aspects

B A Davis, S Allard, A Qureshi et al

British Journal of Haematology 2017, vol 176 (1): 179-191

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Guidelines on red transfusion in sickle cell disease – Part  II: indications for transfusion

B A Davis, S Allard, A Qureshi et al

British Journal of Haematology 2017, vol 176 (1): 179-191

http://onlinelibrary.wiley.com/doi/10.1111/bjh.14383/full

 

Guidelines on neonatal screening and painful vaso-occlusive crisis in sickle cell disease: Associação Brasileira de Hematologia, Hemoterapia e Terapia Celular: Project guidelines: Associação Médica Brasileira – 2016

Braga, Josefina Aparecida Pellegrini et al.

Rev. Bras. Hematol. Hemoter., June 2016, vol.38, no.2, p.147-157

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Clinical and laboratory profile of patients with sickle cell anemia.

Sant’Ana, Phelipe Gabriel dos Santos et al.

Rev. Bras. Hematol. Hemoter., Mar 2017, vol.39, no.1, p.40-4

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Acute crises and complications of sickle cell anemia among patients attending a pediatric tertiary unit in Kinshasa, Democratic Republic of Congo

Michel Ntetani Aloni, Bertin Tshimanga Kadima, Pépé Mfutu Ekulu et al

Hematol Rep. 2017 Jun 1; 9(2): 6952.

https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5472240/

 

A fatal case of immine hyperhemolysis with bone marrow necrosis in a patient with sickle cell disease

Matthew S. Karafin, Arun Singavi, Susan T. Johnson, Joshua J. Field

Hematol Rep. 2017 Feb 23; 9(1): 6934

https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5337824/

 

Hormonal and echocardiographic abnormalities in adult patients with sickle-cell anemia in Bahrain

Taysir S Garadah, Ahmed A Jaradat, Mohammed E Alalawi, Adla B Hassan

J Blood Med. 2016; 7: 283–289

https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5167463/

 

Programa de exercício físico combinado reduz a percepção da dor em paciente com anemia falciforme. Relato de caso.

Botelho, Renata et al

Rev. dor, Sept 2017, vol.18, no.3, p.270-274

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Vivência do preconceito racial e de classe na doença falciforme.

Figueiró, Alessandra Varinia Matte and Ribeiro, Rosa Lúcia Rocha

Saude soc., Mar 2017, vol.26, no.1, p.88-9

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Análise dos gastos das internações hospitalares por anemia falciforme no estado da Bahia

Martins, Maísa Mônica Flores and Teixeira, Martha Carvalho Pereira

Cad. saúde colet 2017, vol 25 (1)

http://www.scielo.br/scielo.php?script=sci_arttext&pid=S1414-462X2017005001106&lng=en&nrm=iso

 

Internações de crianças com doença falciforme no Sistema Único de Saúde no Estado de Minas Gerais,

Fernandes, Ana Paula P.C., Avendanha, Fernanda A. and Viana, Marcos B

  1. Pediatr. (Rio J.), June 2017, vol.93, no.3, p.287-293

http://www.scielo.br/scielo.php?script=sci_arttext&pid=S0021-75572017000300287&lng=en&nrm=iso&tlng=pt

 

Increased prevalence of renal cysts in patients with sickle cell disease

Daveena Meeks, Arunraj Navaratnarajah, Emma Drasar et AL

BMC Nephrol. 2017; 18: 298.

https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5609069/

 

Sickle cell disease and albuminuria: recent advances in our underatanding of sickle cell nephropathy

Vincent Audard, Pablo Bartolucci, Thomas Stehlé

Clin Kidney J. 2017 Aug; 10(4): 475–478.

https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5570022/

 

Telomere length correlates with disease severity and inflammation in sickle cell disease

Colella, Marina Pereira et al.

Rev. Bras. Hematol. Hemoter., June 2017, vol.39, no.2, p.140-145

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Mortality by sickle cell disease in Brazil

Arduini, Giovanna Abadia Oliveira, Rodrigues, Letícia Pinto and Marqui, Alessandra Bernadete Trovó de

Rev. Bras. Hematol. Hemoter., Mar 2017, vol.39, no.1, p.52-56

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Dopplervelocimetria arterial das órbitas em portadores de anemia falciforme: relação com biomarcadores de hemólise. 

Ferrão, Thiago de Oliveira et al

Radiol Bras, Apr 2017, vol.50, no.2, p.103-108

http://www.scielo.br/scielo.php?script=sci_arttext&pid=S0100-39842017000200103&lng=en&nrm=iso&tlng=pt

 

Interleukin-10 haplotypes are not associated with acute cerebral ischemia or high-risk transcranial Doppler in a newborn cohort of 395 children with sickle cell anemia

Belisário, André Rolim et al.

Rev. Bras. Hematol. Hemoter., June 2017, vol.39, no.2, p.108-114

http://www.scielo.br/scielo.php?script=sci_arttext&pid=S1516-84842017000200108&lng=en&nrm=iso

 

Physical activity level and performance in the six-minute walk test of children and adolescents with sickle cell anemia

Melo, Hugo Nivaldo et al.

Rev. Bras. Hematol. Hemoter., June 2017, vol.39, no.2, p.133-139

http://www.scielo.br/scielo.php?script=sci_arttext&pid=S1516-84842017000200133&lng=en&nrm=iso

 

A phase Ib open label, randomized, safety study of SANGUINATE™ in patients with sickle cell anemia

Misra, Hemant et al.

Rev. Bras. Hematol. Hemoter., Mar 2017, vol.39, no.1, p.20-27

http://www.scielo.br/scielo.php?script=sci_arttext&pid=S1516-84842017000100020&lng=en&nrm=iso

 

Comprehensive neuropsychological evaluation of children and adolescents with sickle cell anemia: a hospital-based sample

Nunes, Samantha et al.

Rev. Bras. Hematol. Hemoter., Mar 2017, vol.39, no.1, p.32-39

http://www.scielo.br/scielo.php?script=sci_arttext&pid=S1516-84842017000100032&lng=en&nrm=iso

 

Hydroxyurea therapy in adult Nigerian sickle cell disease: a monocentric survey on patterns of use, clinical effects and patient´s compliance

Adewoyin AS, Oghuvwu OS, Awodu OA.

Afr Health Sci. 2017 , vol;17(1):255-261

https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5636256/

 

Ocular manifestation of sickle cell disease and genetic susceptibility for refractive errors

Shukla P, Verma H, Patel S, Patra PK, Bhaskar LVKS.

Taiwan J Ophthalmol. 2017 , vol 7(2):89-93

https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5602154/

 

Sickle cell retinopathy: improving care with a multidisciplinary approach

Menaa F, Khan BA, Uzair B, Menaa A.

J Multidiscip Healthc. 2017 , vol 10:335-346

https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5587171/

 

Computer-aided classification of sickle cell retinopathy using quantitative features in optical coherence tomography angiography

Minhaj Alam, Damber Thapa, Jennifer I. Lim, Dingcai Cao, Xincheng Yao

Biomed Opt Express. 2017 vol 8(9): 4206–4216

https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5611935/

 

Relationship between ventilation hereogeneity and exercise intolerance in adults with sickle cell anemia

A.J. Lopes, C.L. Marinho, U.D. Alves, C.E.A. Gonçalves, P.O. Silva, E.C. Botelho, R. Bedirian, A.R. Soares, M.C.P. Maioli

Braz J Med Biol Res. 2017; vol 50(8): e651

https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5520223/

 

The intersection between asthma and acute chest syndrome in children with sickle-cell anaemia

Michael R DeBaun, Prof. Robert C Strunk

Lancet. 2016 Jun 18; 387(10037): 2545–2553

https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5041533/

 

Hydroxycarbamine: from an old drug used in malignant hemopathies to a current standard in sickle cell disease

Giovanna Cannas, Solène Poutrel, Xavier Thomas

Mediterr J Hematol Infect Dis. 2017; 9(1): e2017015

https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5333733/

 

Speckle tracking evaluation of right ventricular function in children with sickle cell disease

Tolba OARE, El-Shanshory MR, El-Gamasy MAE, El-Shehaby WA.

Ann Pediatr Cardiol. 2017 vol 10(3):230-233.

https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5594932/

 

Cholelithiasis and its complications in sickle cell disease in a university hospital

Martins, Raquel Alves et al.

Rev. Bras. Hematol. Hemoter., Mar 2017, vol.39, no.1, p.28-31

http://www.scielo.br/scielo.php?script=sci_arttext&pid=S1516-84842017000100028&lng=en&nrm=iso

 

Sickle cell intrahepatic cholestasis unresponsive to exchange blood transfusion: a case report

Guimarães, Juliana Albano de and Silva, Luciana Cristina dos Santos

Rev. Bras. Hematol. Hemoter., June 2017, vol.39, no.2, p.163-166

http://www.scielo.br/scielo.php?script=sci_arttext&pid=S1516-84842017000200163&lng=en&nrm=iso

 

Comprehensive neuropsychological evaluation of children and adolescents with sickle cell anemia: a hospital-based sample.

Nunes, Samantha et al.

Rev. Bras. Hematol. Hemoter., Mar 2017, vol.39, no.1, p.32-39

http://www.scielo.br/scielo.php?script=sci_arttext&pid=S1516-84842017000100032&lng=pt&nrm=iso

 

Novel insights in the management of sickle cell disease in childhood

Lorenzo Iughetti, Elena Bigi, Donatella Venturelli

World J Clin Pediatr. 2016 Feb 8; 5(1): 25–34

https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4737690/

 

Renal papillary necrosis in a patient with sickle cell disease.

Pereira, Benedito Jorge and Andrade, Raquel de

Rev. Bras. Hematol. Hemoter., Sept 2016, vol.38, no.3, p.267-270

http://www.scielo.br/scielo.php?script=sci_arttext&pid=S1516-84842016000300267&lng=en&nrm=iso

 

Oral health-related quality of life of children and teens with sickle cell disease.

Fernandes, Maria Luiza da Matta Felisberto et al.

Rev. Bras. Hematol. Hemoter., June 2016, vol.38, no.2, p.106-112

http://www.scielo.br/scielo.php?script=sci_arttext&pid=S1516-84842016000200106&lng=en&nrm=iso

 

■ . Transient red cell aplasia in two brothers with sickle cell anemia and erythrovirus B19 infection

Furtado, Marina dos Santos Brito Silva et AL

Rev. Bras. Hematol. Hemoter., Sept 2016, vol.38, no.3, p.271-273

http://www.scielo.br/scielo.php?script=sci_arttext&pid=S1516-84842016000300271&lng=en&nrm=iso

 

Relationship between pulmonary and cardiac abnormalities in sickle cell disease: implications for the management of patients.

Maioli, Maria Christina Paixão et al.

Rev. Bras. Hematol. Hemoter., Feb 2016, vol.38, no.1, p.21-27

http://www.scielo.br/scielo.php?script=sci_arttext&pid=S1516-84842016000100021&lng=en&nrm=iso

 

Marcadores de estresse oxidativo em eritrócitos de crianças com doença falciforme

Hermann, Priscila Bacarin et al

  1. Pediatr. (Rio J.), Aug 2016, vol.92, no.4, p.394-399

http://www.scielo.br/scielo.php?script=sci_arttext&pid=S0021-75572016000500394&lng=en&nrm=iso&tlng=pt

 

Determinantes genéticos e Acidente Vascular Encefálico em crianças com doença falciforme

Rodrigues, Daniela O.W. et al

  1. Pediatr. (Rio J.), Dec 2016, vol.92, no.6, p.602-608

http://www.scielo.br/scielo.php?script=sci_arttext&pid=S0021-75572016000700602&lng=en&nrm=iso&tlng=pt

 

 Avaliação de um programa de triagem neonatal para doença falciforme

Eller, Rodrigo and Silva, Denise Bousfield da

  1. Pediatr. (Rio J.), Aug 2016, vol.92, no.4, p.409-413.

http://www.scielo.br/scielo.php?script=sci_arttext&pid=S0021-75572016000500409&lng=en&nrm=iso&tlng=pt

 

Profile of Reproductive Issues Associated with Different Sickle Cell Disease Genotypes

Carvalho, Flávia Anchielle et al.

Rev. Bras. Ginecol. Obstet., Aug 2017, vol.39, no.8, p.397-402

http://www.scielo.br/scielo.php?script=sci_arttext&pid=S0100-72032017000800397&lng=en&nrm=iso&tlng=en

 

Alterações na tomografia computadorizada do tórax em pacientes adultos oligossintomáticos com doença falciforme.

Alves, Ursula David et al

Radiol Bras, Aug 2016, vol.49, no.4, p.214-219

http://www.scielo.br/scielo.php?script=sci_arttext&pid=S0100-39842016000400004&lng=en&nrm=iso&tlng=pt

 

Osteonecrosis, splenic calcifications and sickle cell disease

A K Pannuy, A Lakshman, V Damaraju et al

QJM: An International Journal of Medicine 2017, vol 110 (7): 463-464

https://academic.oup.com/qjmed/article/110/7/463/3066065/Osteonecrosis-splenic-calcification-and-sickle

 

Pathophysiology and treatment of pulmonary hypertension in sickle cell disease

Victor R. Gordeuk, Oswaldo L. Castro, Roberto F. Machado

Blood. 2016 Feb 18; 127(7): 820–828

https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4760088/

 

Review: hemodynamic characteristics and outcomes of sickle cell disease associated pulmonary hypertension

Alem Mehari, Alvin V. Thomas, Alicia N. Thomas, Mark S. Johnson

Ethn Dis. 2016 Autumn; 26(4): 545–552

https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5072484/

 

Acute pain and depressive symptoms: independent predictors of insomnia symptoms among adults with sickle cell disease

Gyasi Moscou-Jackson, Jerilyn Allen, Sharon Kozachik et al

Pain Manag Nurs. 2016 Feb; 17(1): 38–46

https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4769907/

 

Trends in sickle-cell-disease-related priapism in US Children hospitals

Hsin-Hsiao Scott Wang, Katherine W. Herbst et al

Urology. 2016 Mar; 89: 118–122

https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4792742/

 

Neutrophils, platelets, and inflammatory pathways at the nexus of sickle cell disease pathophysiology

Dachuan Zhang, Chunliang Xu, Deepa Manwani, Paul S. Frenette

Blood. 2016 Feb 18; 127(7): 801–809

https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4760086/

 

Interventions for chronic kidney disease in people with sickle cell disease

Noemi BA Roy, Patricia M Fortin, Katherine R Bull et al

Cochrane Database Syst Rev. 2016 Oct; 2016(10): CD012380

https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5360229/

 

Risk factors for mortality in adult patients with cell disease: a meta-analysis of studies in North America and Europe

Poulami Maitra, Melissa Caughey, Laura Robinson et al

Haematologica. 2017 , vol 102(4): 626–636

https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5395103/

 

O processo de consentimento livre e esclarecido nas pesquisas em doença falciforme

Valêncio, Luis Felipe Siqueira and Domingos, Claudia Regina Bonini

Rev. Bioét., Dez 2016, vol.24, no.3, p.469-477

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Coexistência de lúpus eritematoso sistêmico e doença falciforme: relato de caso e revisão da literatura

Robazzi, Teresa Cristina M.V. et al.

Rev. Bras. Reumatol., Fev 2015, vol.55, no.1, p.68-74

http://www.scielo.br/scielo.php?script=sci_arttext&pid=S0482-50042015000100068&lng=en&nrm=iso

 

Allogenic bone narrow transplantation in sickle-cell diseases.

Simões, Belinda Pinto et al.

Rev. Assoc. Med. Bras., Oct 2016, vol.62, suppl.1, p.16-22

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Sobrevida e mortalidade em usuários e não usuários de hidroxiureia com doença falciforme

Araujo, Olinda Maria Rodrigues de et al.

Rev. Latino-Am. Enfermagem, Feb 2015, vol.23, no.1, p.67-73

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Triagem neonatal de hemoglobinopatias no município de São Carlos, São Paulo, Brasil: análise de uma série de casos.

Silva, Camila de Azevedo et al

Rev. paul. pediatr., Mar 2015, vol.33, no.1, p.19-27

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Aleitamento materno e perfil antropométrico de crianças com doença falciforme acompanhadas em serviço de referência em triagem neonatal.

Nogueira, Zeni Drubi et al

Rev. paul. pediatr., June 2015, vol.33, no.2, p.154-159

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Complicações infecciosas em crianças com doença falciforme após esplenectomia cirúrgica.

Monaco Junior, Cypriano Petrus, Fonseca, Patricia Belintani Blum and Braga, Josefina Aparecida Pellegrin

Rev. paul. pediatr., June 2015, vol.33, no.2, p.150-15

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Vitamina D em crianças e adolescentes com doença falciforme: uma revisão integrativa

Oliveira, Jacqueline Faria de et al.

Rev. paul. pediatr., Set 2015, vol.33, no.3, p.349-354

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Sickle-cell anemia and latent diastolic dysfunction: Echocardiographic alterations

Fattori, André et al

Arq. Bras. Cardiol., Apr 2015, vol.104, no.4, p.e30-e33

http://www.scielo.br/scielo.php?script=sci_arttext&pid=S0066-782X2015000400012&lng=en&nrm=iso

 

■ by Dr Paulo Fernando Leite

Cardiologia – Centro Médico Unimed BH

Rua Gonçalves Dias 202

Belo Horizonte/MG/Brasil

31 30033306       /   40204020

CRMMG: 7026

Email: pfleite1873@gmail.com